Congenital Hepatic Fibrosis and Need for Liver Transplant

B. Geramizadeh, P. Keramati, A. Bahador, H. Salahi, S. Nikeghbalian, S. M. Dehghani, S. A. Malek-Hosseini

ABSTRACT

histopathology of the explanted hepatectomy specimen revealed congeni­tal hepatic fibrosis. To the best of our knowledge, coexistence of hepatic failure and cirrhosis in congenital hepatic fibrosis, have not yet been reported in the English literature.

 congenital hepatic fibrosis (CHF) refers to a unique liver histology character­ized by bland portal fibrosis, prolifera­tion of interlobular bile ducts in the portal areas with variable shapes and sizes of bile ducts